INTRODUCTION

Arrhythmogenic right ventricular cardiomyopathy is a rare heart-muscle disorder characterized by progressive replacement of right ventricular myocardium by fibrofatty tissue. Noncompaction of the ventricular myocardium is also rare congenital cardiomyopathy, characterized by an arrest in intrauterine endomyocardial morphogenesis. We present an extremely rare patient who presented with incessant ventricular tachycardia and who had both of these two cardiomyopathies at the same time.