Sickle Cell Disease

Priapism in Homozygous Sickle Cell Disease: A 40-year Study of the Natural History

Issue:

Vol 64, Issue 3: June (2015)

DOI:

10.7727/wimj.2014.119

Pages:

175–80

Synopsis:

The authors report on the incidence, pattern, natural history and outcome of priapism in 162 male patients with homozygous sickle cell (SS) disease who have been followed from birth for periods up to 40 years.

ABSTRACT

Objectives: To describe the incidence, pattern, and outcome of priapism in homozygous sickle cell (SS) disease.

Methods: Regular review, for periods up to 40 years was done, of all 162 males with SS disease detected during the screening of 100 000 consecutive non-operative deliveries at the main government maternity hospital in Kingston, Jamaica, between June 1973 and December 1981.

Received:

19 May, 2014

Revised:

05 Jun, 2014

Accepted:

05 Jun, 2014

PDF Attachment:

wimjjun2015_175_180.pdf

Journal Sections:

Keywords:

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e-Published: 27 Apr, 2015

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Clinical Factors Associated With Morbidity and Mortality in Patients Admitted with Sickle Cell Disease

Issue:

Vol 63, Issue 7: Dec (2014)

DOI:

10.7727/wimj.2014.012

Pages:

711–6

Synopsis:

Sickle cell disease still carries a high morbidity and mortality in patients admitted to hospital. Recurrent admissions are a concern, as this impact on patient’s morbidity and quality of life.

ABSTRACT

Objective: To determine the clinical factors associated with the length of hospitalization and mortality in patients with sickle cell disease (SCD).

Received:

03 Feb, 2014

Accepted:

28 Feb, 2014

PDF Attachment:

wimjdec2014_711_716.pdf

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e-Published: 05 Mar, 2015

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Dural Venous Sinus Thrombosis in Sickle Cell Disease in a West Indian

Issue:

Vol 63, Issue 7: Dec (2014)

DOI:

10.7727/wimj.2014.002

Pages:

811–2

The Editor,

Sir,

Intracranial neurovascular manifestations in sickle cell disease include cerebral infarction, parenchymal and epidural haemorrhage, subarachnoid haemorrhage with single or multiple aneurysms, Moyamoya syndrome and posterior reversible ischemic encephalopathy.

Received:

05 Feb, 2014

Accepted:

12 Feb, 2014

PDF Attachment:

wimjdec2014_811_812.pdf

Journal Sections:

Letters to the Editor

Keywords:

Sickle Cell Disease

Haemoglobin

Dural venous sinus thrombus

Journal Authors:

e-Published: 03 Sep, 2014

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A Survey of the Pain Management of Acute Painful Crisis among Patients with Sickle Cell Disease at Two Centres in Jamaica

Issue:

Vol 63, Issue 3: Emergency Medicine (2014)

DOI:

10.7727/wimj.2013.333

Pages:

252–7

Synopsis:

Evidence suggests that acute painful crisis (APC) can be managed safely and effectively in the outpatient setting. This survey reviewed the management of APC at two outpatient centres on the Mona campus of the University of the West Indies.

ABSTRACT

Objectives: The aim of this survey was to establish the pain management approaches to acute painful crisis (APC) in sickle cell patients at two healthcare facilities and to compare with available guidelines.

Received:

09 Dec, 2013

Accepted:

12 Feb, 2014

PDF Attachment:

augier_et_al-management_of_painful_crisis_in_sickle_cell_patients.pdf

Journal Sections:

Keywords:

Journal Authors:

e-Published: 12 Jun, 2014

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The Use of Analgesic Drugs in Patients with Sickle Cell Painful Crisis

Issue:

Vol 63, Issue 5: Sep (2014)

DOI:

10.7727/wimj.2012.272

Pages:

479–83

Synopsis:

Painful crisis in patients with sickle cell anaemia is associated with severe pain in 75% and most will require second line therapy for adequate resolution. Physicians need to provide adequate pain relief to decrease morbidity in these patients.

ABSTRACT

Objective: To determine the drug options used for pain in patients with acute sickle cell painful crisis at the University Hospital of the West Indies (UHWI), Jamaica.

Method: This retrospective study assessed all patients admitted to the UHWI between January 1, 2006 and December 31, 2010 with acute sickle cell anaemia painful crisis and the data obtained regarding site, severity, outcome and drug options selected for pain.

Received:

08 Oct, 2012

Revised:

24 Feb, 2013

Accepted:

12 Mar, 2013

PDF Attachment:

boyd_et_al-analgesic_drugs_and_sickle_cell_anaemia.pdf

Journal Sections:

Keywords:

Journal Authors:

e-Published: 30 Apr, 2014

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A Technique for Mitral Valve Surgery in Sickle Cell Disease

Issue:

Vol 63, Issue 2: Mar (2014)

DOI:

10.7727/wimj.2013.280

Pages:

204–5

INTRODUCTION

Received:

09 Oct, 2013

Accepted:

30 Oct, 2013

PDF Attachment:

smith_et_al-mitral_valve_surgery_in_sickle_cell_disease.pdf

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e-Published: 11 Apr, 2014

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Diagnostic Accuracy of Spot and Timed Measurements of Urinary Albumin Concentration to Determine Microalbuminuria in Sickle Cell Disease

Issue:

Vol 62, Issue 9: Dec (2013)

DOI:

10.7727/wimj.2012.323

Synopsis:

We report that in sickle cell disease, both spot and two-hour timed urine collections for measurements of albumin concentration or albumin:creatinine ratios are good proxy measures of total 24-hour albumin excretion. These much simpler, and likely more cost-effective, methods can be applied in clinical practice with confidence.

ABSTRACT

Objective: Whereas measurement of albumin:creatinine ratio (ACR) in spot urine samples is indicated for determining microalbuminuria, its performance or that of urinary albumin excretion rate (UAER) in predicting microalbuminuria in sickle cell disease (SCD) is unclear. We therefore tested the diagnostic performance of these measures in spot and timed urine samples in predicting a UAER in 24-hour samples.

Received:

29 Nov, 2012

Revised:

26 Jun, 2013

Accepted:

04 Sep, 2013

PDF Attachment:

asnani_and_reid-spot_and_timed_uac_in_scd.pdf

Journal Sections:

Original Articles

Keywords:

Sickle Cell Disease

Albumin:creatinine ratio

diagnostic accuracy

microalbumin measurement

renal disease

urinary albumin concentrations

Journal Authors:

MR Asnani

ME Reid

e-Published: 29 Nov, 2013

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Pre-published Manuscript

This manuscript has been assigned to a volume and issue but has not yet been published. It is either being edited, typeset or is in the proof stage of publication.
In the pre-published stage, this manuscript may contain statements, opinions, and information that have errors in facts, figures, or interpretation. Any final changes in this manuscript will be made at the time of publication and will be reflected in the final electronic version of the issue. The editors and authors and their respective employees are not responsible or liable for the use of any such inaccurate or misleading data, opinion or information contained in the articles in this section.

Subjective Well-being of Adults with Homozygous Sickle Cell Disease in Jamaica

Issue:

Vol 60, issue 2 (2011)

Pages:

181–7

Synopsis:

Advances in treatment of sickle cell disease have improved the prognosis for patients. As these patients are living longer, issues of subjective well-being become important. Past studies have mostly focussed on patients’ negative life experiences. This study examines both patients’ positive and negative experiences, as well as their satisfaction with life.

ABSTRACT

Objectives: This study compared the subjective well-being of adults with homozygous sickle cell (SS) disease to a matched group of healthy adult peers. The differential influence of sociodemographic factors on the subjective well-being of Sickle Cell patients was also examined.

PDF Attachment:

dr_thomas_wimj.qxd_.pdf

Journal Sections:

Keywords:

subjective well-being

quality of life.

Journal Authors:

JA Thomas

GE Lipps

e-Published: 17 Oct, 2013

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Pattern of Pregnancy Weight Gain in Homozygous Sickle Cell Disease and effect on Birth Size

Issue:

Vol 60, issue 1 (2011)

Pages:

36–40

Synopsis:

Maternal weight gain between 25–30 weeks gestation correlates positively with birthweight among AA mothers but appears delayed beyond 30 weeks in SS mothers.

ABSTRACT

Objective: To assess pregnancy weight gain and newborn anthropometry in mothers with homozygous sickle cell (SS) disease and normal controls.

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Keywords:

Journal Authors:

e-Published: 17 Oct, 2013

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Jamaica, the Caribbean and Sickle Cell Disease

Issue:

Vol 61, issue 4 (2012) - Special Issue on Jamaica and Trinidad and Tobago 50 years Independence

Pages:

331–7

Synopsis:

The development of research interests in sickle cell disease has been traced from the first recorded case, the founding of the University Hospital of the West Indies and the Jamaica Sickle Cell Unit with its worldwide influence on clinical practice in this disease.

ABSTRACT

The development of research interests in sickle cell disease has been traced from the first recorded case, the founding of the University Hospital of the West Indies and the Jamaican Sickle Cell Unit with its influence on clinical practice in this disease worldwide.

PDF Attachment:

dr_gr_serjeant_wimj.qxd_.pdf

Journal Sections:

Keywords:

prevention of sickle cell disease

Journal Authors:

GR Serjeant

e-Published: 21 Aug, 2013

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ISSN: 2309-5830